This study tried to identify new environmental triggers or genetic causes in heritable pulmonary arterial hypertension. They found several potential genes for further exploration, but they also found consistent toxin exposure on one of the families they were investigating. They conclude that environmental triggers should also be investigated in heritable PAH. Read the Scientific Reports article

This study identified factors associated with a delayed diagnosis of PAH and found that earlier diagnosis (<6 months) and treatment initiation were associated with significantly improved survival. More early diagnosis patients saw a pulmonologist before another provider. Read the Pulmonary Circulation article

A review of 12 studies evaluating selexipag in pediatric patients with pulmonary arterial hypertension found that it improved functional capacity and mPAP, especially when added to existing therapies. About 60% of pediatric patients had side effects, mostly mild. Read the Pediatric Cardiology article